Successfully Treated Epstein-Barr Virus (Ebv) Associated Hemophagocytic Lymphohistiocytosis (Hlh) With Pulse Steroid

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a rare disease with fatal progression This disease has two types familial and secondary HLH Both of them have the same clinical spectrum Fever hepatosplenomegaly pancytopenia lymphadenopathy are the most observed signs and symptoms In this article 18 months old girl who was diagnosed with Epstein Barr vino associated HLH and successfully treated with only pulse steroid is presented to emphasize that pulse steroid can be effective in EBV associated HLH Therefore this agent may be used at the beginning of this diagnosis instead of commonly practiced HLH 2004 chemotherapy protocol