Naevus Comedonicus Syndrome With Bilateral Congenital Cataract and Arachnoid Cyst

Abstract

Naevus comedonicus syndrome (NCS) is a rare syndrome with extracutaneous findings. Dilated follicular ostiums plugged with keratinous material are seen in naevus comedonicus. NCS may occur with ocular, skeletal, and central nervous system symptoms. We present this rare case of NCS which presented with bilateral blaschkoid cutaneous involvement, bilateral congenital cataract and arachnoid cyst.